Ebstein’s anomaly and Left Ventricular Non Compaction Cardiomyopathy: a Not So Unusual Association

Daniele Andreini, Gianluca Pontone, Saima Mushtaq, Emanuela Muratori, Marco Guglielmo, Edoardo Conte, Patrizia Carita', Mauro Pepi

Abstract


Left ventricular non-compaction (LVNC) is a rare congenital cardiomyopathy. It is thought to be a congenital arrest of endomyocardial embryogenesis in utero. It has been reported the association with other cardiac abnormalities. We presented two cases of association of LVNC and Ebstein's anomaly. The cardiac magnetic resonance (CMR) allows a comprehensive evaluation of associated findings. All patients with Ebstein’s anomaly should be carefully evaluated for LVNC. The prompt identification of myocardial non compaction is important because of its high mortality due to progressive heart failure, tromboembolism and malignant arrhythmias


Keywords


Ebstein's anomaly, Left ventricle non compaction, CMR, imaging.

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DOI: https://doi.org/10.17987/icfj.v8i0.288

Copyright (c) 2016 Daniele Andreini, Gianluca Pontone, Saima Mushtaq, Emanuela Muratori, Marco Guglielmo, Patrizia Carita', Mauro Pepi

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