Rupture of Aneurysm of Valsalva Sinus and Aortopathy in Bicuspid Aortic Valve: A Case Report and Review of Literature

Patrizia Carità, Massimo Verdecchia, Elisabetta Mancini, Giovanni Ferro, Marco Guglielmo, Egle Corrado, Salvatore Novo, Mauro Pepi, Gianluca Pontone

Abstract


The bicuspid aortic valve is one of the most common forms of congenital heart defect. It is a complex entity, in which involvement of the thoracic aorta forms part of the disease spectrum. The ascending aorta is the most common site involved in this process. We report the extremely rare case of a patient with true BAV associated with a diffuse aortopathy, involving the aneurysm of the non coronary sinus, that suddenly rupted into the right atrium and required urgent cardiac surgery, and the aneurismal dilation of a (non aberrant) left subclavian artery, resembling a Kommerell’s diverticulum. 


Keywords


bicuspid aortic valve, valsalva sinus aneurysm, echocardiography, cardiac CT

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DOI: https://doi.org/10.17987/icfj.v8i0.289

Copyright (c) 2016 Patrizia Carità, Massimo Verdecchia, Emanuela Mancini, Giovanni Ferro, Marco Guglielmo, Egle Corrado, Salvatore Novo, Mauro Pepi, Gianluca Pontone

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